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Table 1 Rating scales used for eye closing, eye opening, and procerus/corrugator supercilii contractions

From: Upper facial chorea in Huntington disease

Score

0

1

2

3

4

Eye closing

Rare or absent eyeblinks

Normal rate of blinking

Fast rate of eye blinks

Continuous repetitive blinking

Blepharospasm

Eye opening

Eyes partially closed

Normal eye opening

Moderately increased frequency of eye openings

Markedly enlarged palpebral fissure but without eyebrow elevation or frontalis contractions

Markedly enlarged palpebral fissure with marked eyebrow elevation and frontalis contractions

Procerus

Absent

Rare

Frequent

Continuous

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